Portopulmonary hypertension in liver disease presenting in. Poph in the 14 patients was based on rightsided heart catheterization displaying mean pulmonary artery pressure mpap 25 mmhg, indexed pulmonary vascular resistances 3 wood units m2, and pulmonary wedge pressure hospital s local committee on clinical investigation. Evaluation of a program of pharmaceutical counseling for. Survival appeared to be substantially better than that still observed today in sscpah, in which estimated 3year survival is about 50%. Regional right ventricular rv dysfunction rrvd is an echocardiographic feature in acute pulmonary embolism pe, primarily reported in patients with moderatetosevere rv dysfunction. How pregnancy impacts adult cyanotic congenital heart. Disponible en ligne depuis le mardi 30 juillet 2019 fourdimensional flow magnetic resonance imaging in cardiovascular diseases. Automatic recognition of abnormal respiratory events during sleep by a pacemaker transthoracic impedance sensor. Automatic recognition of abnormal respiratory events.
Balloon pulmonary angioplasty in a patient with chronic. Late outcomes of transcatheter aortic valve replacement in. We set up a pharmaceutical counseling program for both direct oral anticoagulant and vitamin k antagonist drugs in our hospital in 2015. Surgery of single ventricles in humanitarian practice. However, national data regarding procedural characteristics and clinical outcomes over time are limited. Results description of the foetal cohort between january, 2002 and december, 2011, 2464 foetal heart defects were referred to us for expertise. Generally, banding was selected for young children who had clinical pulmonary overflow without valvular insufficiency. A ventricular septal defect vsd is an integral part of most congenital heart defects chd.
In addition to the risk of multiple organ failure and death, cardiogenic shock is sometimes associated with cardiorenal syndrome oliguria, increased urea and creatinine levels concomitant with myocardial failure, which leads to longer hospital stays, the need for circulatory support, and an increased death rate. Percutaneous left atrial appendage closure is a reasonable. Clinical outcomes of pulmonary arterial hypertension in. Anatomy of the ventricular septal defect in congenital. Prevention of inappropriate shocks in icd recipients. Idiopathic pulmonary arterial hypertension ipah is a complex disease associated with vascular remodeling and a proliferative disorder in pulmonary artery smooth muscle cells pasmcs that has been variably described as having neoplastic features. Description of modern practices of percutaneous coronary. However, survival and the incidence of severe complications have been assessed in relatively small populations andor with limited followup. Linnovation organisationnelle et technologique sont au c. Department of thoracic and vascular surgery, marie lannelongue hospital. Objective there is growing evidence that maternal mortality in pregnant women with pulmonary arterial hypertension associated with congenital heart disease pahchd is lower than that in available data.
He obtained his masters of science and phd degree in 2000 in the laboratory of surgical research at marie lannelongue hospital and paris sud university. Hopitalmarielannelongue, le plessisrobinson, france. A 77 yearold woman was admitted in our hospital because of faintness, dizziness and nausea with a suspected inferior. Objectives the aim of this study was to assess nationwide performance trends and clinical outcomes of tavr during a 6year period. However, ph remains an incurable condition with a high mortality rate, underscoring the need for a. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. Radiology, marielannelongue hospital, le plessisrobinson, france p. Cardiology, leiden university medical center, leiden, the netherlands.
Department of pediatric cardiac surgery, marie lannelongue hospital, le plessis robinson, france research areas. We report the first french case of percutaneous balloon pulmonary angioplasty bpa in a 78yearold patient with chronic thromboembolic pulmonary hypertension cteph. There is increasing interest in registry data to get a clear picture of contemporary practice in various fields, however many existing registries have significant limitations. Unique predictors of mortality in patients with pulmonary arterial hypertension associated with systemic sclerosis in the reveal registry. We identified consecutive patients admitted to the emergency department between 1999. Regional right ventricular dysfunction in acute pulmonary. Experts recommendations for the management of cardiogenic. Pulmonary hypertension service, royal brompton hospital. Operator and hospital volumeoutcome relationship in patients undergoing elective. Pulmonary arterial hypertension associated with systemic. This study investigated the clinical importance of rrvd by assessing its relationship with clot burden and biomarkers. Background oral anticoagulants are widely used for treatment and prevention of thromboembolic diseases.
Temporal trends in transcatheter aortic valve replacement. Image in cardiovascular medicine demonstration of a. Pdf electrical cardiometry in patients with congenital. Loss of kcnk3 is a hallmark of rv hypertrophydysfunction. Backgroundpercutaneous left atrial appendage laa closure is an emerging option for patients with atrial fibrillation at high risk for cerebrovascular events. Effect of aleglitazar on cardiovascular outcomes after acute coronary syndrome in patients with.
Monitoring of circulation and cardiac output is a priority in the paediatric. The patient had a history of acute pulmonary embolism in 2004 with recurrence in 2011. A 77 yearold woman was admitted in our hospital because of faintness, dizziness and nausea with a suspected inferior myocardial infarction on electrocardiogram. In 2005, he complemented his training by obtaining a fellowship in thoracic surgery and lung transplantation at the toronto general hospital, university of toronto, canada. Pneumology departments, university hospital, grenoble, france. Background transcatheter aortic valve replacement tavr is standard therapy for patients with severe aortic stenosis who are at high surgical risk. Longterm outcomes after percutaneous closure of ostium. Methods women with pahchd followed in seven french referral centres were retrospectively. To determine the prevalence of vsd in various types of chd and the distribution of their anatomic types. Background transcatheter aortic valve replacement tavr has revolutionized management of highrisk patients with severe aortic stenosis.
Objectives this report details late clinical outcome and its determinants in the france2 french aortic national. Clinical and translational research has played a major role in advancing our understanding of pulmonary hypertension ph, including pulmonary arterial hypertension and other forms of ph with severe vascular remodelling e. Pathology and pathobiology of pulmonary hypertension. At the end of 2012, he complained of persistent dyspnoea and cteph was diagnosed on lung radionuclide.
Finally, there were 1592 live births, 799 terminations of pregnancy, and 73 in utero foetal deaths. Pulmonary hypertension in chronic heart failure wiley online library. Clinical outcomes of pulmonary arterial hypertension in patients carrying an acvrl1 alk1 mutation barbara girerd, david montani, florence coulet4, benjamin sztrymf2, azzeddine yaici2, xavier ja. Goaloriented therapy, also known as treattotarget therapy, is recommended in the european society of cardiology esceuropean respiratory society ers guidelines for the diagnosis and treatment of pulmonary hypertension 1, 2. Interventional radiology, marielannelongue hospital, le plessisrobinson, france p. Grenoble, poitiers, pessac, metz, le plessis robinson, mulhouse, vandoeuvrelesnancy and saintetienne. Le plessis robinson et lhopital europeen georges pompidou, paris coordonnateur. Acha travel directory adult congenital heart association.
Improving quality of congenital heart disease research in canada. In order to evaluate this hypothesis, we collected data of pregnancies in women with pahchd. During the morphologic study a special attention was. Impact of anatomic characteristics and initial biventricular surgical strategy on outcomes in various forms of doubleoutlet right ventricle olivier villemain, md,a emre belli, md,b magalie ladouceur, md,a lucile houyel, md,b zakaria jalal, md,a virginie lambert, md, phd,c mohamed ly, md,b pascal vouhe, md, phd,a and damien bonnet, md, phda abstract. Objective evaluate patient satisfaction and the evolution of their knowledge throughout the pharmaceutical counseling program. Archives of cardiovascular diseases supplements sous presse. To decode the phenotype of pasmcs in ipah, pasmcs from explanted lungs of patients with ipah ipahpasmcs and from controls cpasmcs were. Adult congenital cardiology clinic at university of.
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